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Managing familial chylomicronemia syndrome (FCS) requires a focus on low-fat nutrition

Dietary fat restriction has been the cornerstone of FCS management. Patients are advised to limit dietary fat intake to less than 15–20 g/day (approximately 1 tablespoon of olive oil) or less than 10–15% of total daily caloric intake.34

People with FCS should also avoid drinking alcohol and limit consumption of simple carbohydrates.

Adhering to such a diet is very difficult for 
many patients, but extensive practical 
suggestions are available.

1 Tablespoon of Olive Oil

Referring patients to a registered dietitian 
nutritionist (RDN) with an understanding of FCS is often a critical aspect of managing the condition.

KnowYourTGs.com: Built for patients

We’ve created a patient-friendly site packed with FCS nutritional guidelines and recipes to help your patients take a proactive role in managing their condition. Why not share it with your patients who have FCS today? Topics include:

  • How to work with a registered dietitian nutritionist (RDN)

  • Fact sheets about nutrition, cooking, reading food labels, and related topics

  • Information about specific dietary fats, such as the role of medium-chain triglycerides (MCTs)

  • Resources for tracking daily fat consumption

  • A free Patient Guide to FCS

    Low-fat Recipes
KnowYourTGs.com on tablet device

Additional nutrition support details

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Further reading 

Williams L, Rhodes KS, Karmally W, Welstead LA, Alexander L, Sutton L. Familial chylomicronemia syndrome: Bringing to life dietary recommendations throughout the life span. J Clin Lipidol. 2018;12(4):908-19. 

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REFERENCES

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